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Displaying diseases 326 - 350 of 660 in total
Hyperekplexia  (149400 )
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
gamma-Aminobutyric acid (HMDB0000112) Cerebrospinal Fluid (CSF)0.011 uMAbnormalNewborn (0-30 days old)Female details
Hyperglycinemia, lactic acidosis, and seizures  (614462 )
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
Lactic acid (HMDB0000190) Blood4600-57700 uMAbnormalNewborn (0-30 days old)Male details
Glycine (HMDB0000123) Blood906 uMAbnormalNewborn (0-30 days old)Male details
Hyperinsulinemic hypoglycemia, familial, 1, HHF1  (256450 )
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
D-Glucose (HMDB0000122) Blood1940 +/- 570 uMAbnormalChildren (1-13 years old)Both details
D-Glucose (HMDB0000122) Blood1900 +/- 700 uMAbnormalChildren (1-13 years old)Both details
D-Glucose (HMDB0000122) Blood600-1000 uMAbnormalNewborn (0-30 days old)Both details
alpha-D-Glucose (HMDB0003345) Blood600-1000 uMAbnormalNewborn (0-30 days old)Both details
alpha-D-Glucose (HMDB0003345) Blood1940 +/- 570 uMAbnormalChildren (1-13 years old)Both details
alpha-D-Glucose (HMDB0003345) Blood1900 +/- 700 uMAbnormalChildren (1-13 years old)Both details
Hyperinsulinism-hyperammonemia syndrome  (606762 )
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
Oxoglutaric acid (HMDB0000208) Urine100-166 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Oxoglutaric acid (HMDB0000208) Urine149-247 umol/mmol creatinineAbnormalChildren (1-13 years old)Female details
Oxoglutaric acid (HMDB0000208) Urine15-107 umol/mmol creatinineAbnormalChildren (1-13 years old)Female details
Hyperlipoproteinemia  (238600 )
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
D-Glucose (HMDB0000122) Blood5114.0 +/- 483.0 uMAbnormalAdult (>18 years old)Both details
Cholesterol (HMDB0000067) Blood<5172.590 uMAbnormalAdult (>18 years old)Both details
Cholesterol (HMDB0000067) Blood2680 +/- 1850 uMAbnormalAdult (>18 years old)Not Available details
alpha-D-Glucose (HMDB0003345) Blood5114.0 +/- 483.0 uMAbnormalAdult (>18 years old)Both details
Hyperlysinemia I, familial  (238700 )
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
Lysine (HMDB0000182) Blood1208-1472 uMAbnormalChildren (1-13 years old)Both details
Pipecolic acid (HMDB0000070) Cerebrospinal Fluid (CSF)24-33 uMAbnormalChildren (1-13 years old)Both details
Lysine (HMDB0000182) Urine1384-1742 umol/mmol creatinineAbnormalChildren (1-13 years old)Both details
Ornithine (HMDB0000214) Urine26-63 umol/mmol creatinineAbnormalChildren (1-13 years old)Both details
L-Arginine (HMDB0000517) Urine120-221 umol/mmol creatinineAbnormalChildren (1-13 years old)Both details
Homocitrulline (HMDB0000679) Urine63-83 umol/mmol creatinineAbnormalChildren (1-13 years old)Both details
Hyperlysinuria  (247950 )
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
Lysine (HMDB0000182) Urine1413.757 umol/mmol creatinineAbnormalChildren (1-13 years old)Female details
Lysine (HMDB0000182) Urine2050-18736 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
L-Cystine (HMDB0000192) Urine908-5585 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Ornithine (HMDB0000214) Urine190-9883 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
L-Arginine (HMDB0000517) Urine54-8426 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Hypermanganesemia with dystonia 1  (613280 )
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
Manganese (HMDB0001333) Blood3.285 uMAbnormalChildren (1-13 years old)Female details
Manganese (HMDB0001333) Blood1.511-14.973 uMAbnormalChildren (1-13 years old)Male details
Manganese (HMDB0001333) Blood3.48 uMAbnormalChildren (1-13 years old)Male details
Hypermanganesemia with dystonia 2  (617013 )
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
Manganese (HMDB0001333) Blood0.963-3.830 uMAbnormalChildren (1-13 years old)Both details
Hypermethioninemia  (613752 )
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
L-Tyrosine (HMDB0000158) Blood108-146 uMAbnormalChildren (1-13 years old)Female details
L-Tyrosine (HMDB0000158) Blood48-95 uMAbnormalChildren (1-13 years old)Female details
Methionine (HMDB0000696) Blood20-273 uMAbnormalNewborn (0-30 days old)Both details
Methionine (HMDB0000696) Blood230-1000 uMAbnormalChildren (1-13 years old)Female details
Methionine (HMDB0000696) Blood37-400 uMAbnormalChildren (1-13 years old)Female details
Betaine (HMDB0000043) Blood211 uMAbnormalChildren (1-13 years old)Male details
Creatine (HMDB0000064) Blood528 +/- 42 uMAbnormalChildren (1-13 years old)Male details
L-Cystathionine (HMDB0000099) Blood0.552 uMAbnormalChildren (1-13 years old)Male details
Methionine (HMDB0000696) Blood477-784 uMAbnormalChildren (1-13 years old)Male details
Hyperornithinemia with Gyrate Atrophy  (258870 )
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
Ornithine (HMDB0000214) Blood1066(798-1321) uMAbnormalAdult (>18 years old)Both details
Ornithine (HMDB0000214) Cerebrospinal Fluid (CSF)288(240-314) uMAbnormalAdult (>18 years old)Both details
Hyperornithinemia-hyperammonemia-homocitrullinuria  (238970 )
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
Orotic acid (HMDB0000226) Urine59-282 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Hyperoxalemia
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
Ascorbic acid (HMDB0000044) Blood39.0 +/- 92.7 uMAbnormalAdult (>18 years old)Both details
Ascorbic acid (HMDB0000044) Blood6.5 +/- 18.6 uMAbnormalAdult (>18 years old)Both details
Citric acid (HMDB0000094) Blood141.3 +/- 54.7 uMAbnormalAdult (>18 years old)Both details
Citric acid (HMDB0000094) Blood117.6 +/- 37.2 uMAbnormalAdult (>18 years old)Both details
Creatinine (HMDB0000562) Blood40.3 +/- 14.5 uMAbnormalAdult (>18 years old)Both details
Hyperphosphatasia  (239000 )
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
Calcium (HMDB0000464) Blood2120.864 uMAbnormalChildren (1-13 years old)Female details
Phosphate (HMDB0001429) Blood315.885 uMAbnormalChildren (1-13 years old)Female details
25-Hydroxyvitamin D2 (HMDB0001438) Blood24233.741 uMAbnormalChildren (1-13 years old)Female details
Hyperpipecolatemia
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
Pipecolic acid (HMDB0000070) Cerebrospinal Fluid (CSF)1-2 uMAbnormalChildren (1-13 years old)Male details
Pipecolic acid (HMDB0000070) Urine4.522 umol/mmol creatinineAbnormalChildren (1-13 years old)Male details
Hyperprolinemia, type I  (239500 )
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
Proline (HMDB0000162) Blood208.459-1745.845 uMAbnormalChildren (1-13 years old)Both details
Hyperprolinemia, type II  (239510 )
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
Proline (HMDB0000162) Blood>1500 uMAbnormalChildren (1-13 years old)Not Specified details
Hypertension  (145500 )
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
Angiotensin III (HMDB0001036) Blood0.0000215 +/- 0.0000022 uMAbnormalAdult (>18 years old)Both details
Angiotensin II (HMDB0001035) Blood0.0000574 +/- 0.0000030 uMAbnormalAdult (>18 years old)Both details
m-Tyramine (HMDB0004989) Blood0.00034 +/- 0.0000875 uMAbnormalAdult (>18 years old)Both details
p-Synephrine (HMDB0004826) Blood0.0009 +/- 0.0004 uMAbnormalAdult (>18 years old)Both details
(R)-Salsolinol (HMDB0005199) Blood0.0010 +/- 0.00043 uMAbnormalAdult (>18 years old)Both details
p-Octopamine (HMDB0004825) Blood0.00036 +/- 0.000065 uMAbnormalAdult (>18 years old)Both details
Eicosapentaenoic acid (HMDB0001999) Blood11.0 +/- 7.3 uMAbnormalAdult (>18 years old)Both details
Zinc (HMDB0015532) Blood14.9 +/- 5.0 uMAbnormalAdult (>18 years old)Both details
Docosahexaenoic acid (HMDB0002183) Blood64.7 +/- 39.2 uMAbnormalAdult (>18 years old)Both details
alpha-Linolenic acid (HMDB0001388) Blood21.2 +/- 7.2 uMAbnormalAdult (>18 years old)Both details
Arachidonic acid (HMDB0001043) Blood34.3 +/- 27.8 uMAbnormalAdult (>18 years old)Both details
Linoleic acid (HMDB0000673) Blood175.9 +/- 65.0 uMAbnormalAdult (>18 years old)Both details
20-Hydroxyeicosatetraenoic acid (HMDB0005998) Blood0.0028 (0.0012-0.0067) uMAbnormalAdult (>18 years old)Both details
Aldosterone 18-glucuronide (HMDB0010345) Urine0.001 (0.00034-0.0022) umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Dihydrouracil (HMDB0000076) Urine2.4 +/- 1.67 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Uracil (HMDB0000300) Urine6.00 +/- 4.00 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Hyperthyroidism
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
3,5-Diiodo-L-tyrosine (HMDB0003474) Blood0.0036 (0.0010-0.0134) uMAbnormalAdult (>18 years old)Both details
2-Oxoarginine (HMDB0004225) Blood0.160 +/- 0.009 uMAbnormalAdult (>18 years old)Both details
Thyroxine sulfate (HMDB0002728) Blood0.000033 +/- 0.000010 uMAbnormalAdult (>18 years old)Both details
L-Thyronine (HMDB0000667) Urine0.0069 +/- 0.0014 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
3,5-Diiodothyronine (HMDB0000582) Urine0.000086 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Liothyronine (HMDB0000265) Urine0.00075 +/- 0.00033 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Hypervalinemia  (277100 )
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
L-Valine (HMDB0000883) Blood1495-1675 uMAbnormalChildren (1 - 13 years old)Both details
L-Valine (HMDB0000883) Urine18.246-18.720 umol/mmol creatinineAbnormalChildren (1 - 13 years old)Both details
Hyperzincaemia and hypercalprotectinaemia  (194470 )
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
Copper (HMDB0000657) Blood25.0842 uMAbnormalChildren (1 - 13 years old)Female details
Zinc (HMDB0015532) Blood150.927 uMAbnormalChildren (1 - 13 years old)Female details
Hypobetalipoproteinemia
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
Glucosylceramide (HMDB0000140) Blood0.39 +/- 0.065 uMAbnormalAdult (>18 years old)Both details
LacCer(d18:1/12:0) (HMDB0004866) Blood2.5 (2.7-2.8) uMAbnormalAdult (>18 years old)Both details
Trihexosylceramide (d18:1/12:0) (HMDB0004877) Blood0.9 (1.0-0.9) uMAbnormalAdult (>18 years old)Both details
Trihexosylceramide(d18:1/18:0) (HMDB0004880) Blood0.9 (1.0-0.9) uMAbnormalAdult (>18 years old)Both details
Trihexosylceramide(d18:1/22:0) (HMDB0004882) Blood0.9 (1.0-0.9) uMAbnormalAdult (>18 years old)Both details
Trihexosylceramide (d18:1/24:0) (HMDB0004886) Blood0.9 (0.9-1.0) uMAbnormalAdult (>18 years old)Both details
Trihexosylceramide (d18:1/26:1(17Z)) (HMDB0004884) Blood0.9 (0.9-1.0) uMAbnormalAdult (>18 years old)Both details
Tetrahexosylceramide (d18:1/12:0) (HMDB0004958) Blood1.0 (1.0-1.1) uMAbnormalAdult (>18 years old)Both details
Ganglioside GM3 (d18:1/16:0) (HMDB0004844) Blood4.0 (4.3-4.5) uMAbnormalAdult (>18 years old)Both details
Hypoglycemia, familial neonatal  (240800 )
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
D-Glucose (HMDB0000122) Blood1665.224-2775.374 uMAbnormalInfant (0-1 year old)Female details
alpha-D-Glucose (HMDB0003345) Blood1665.224-2775.374 uMAbnormalInfant (0-1 year old)Female details
Hypogonadism  (146110 )
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
Testosterone (HMDB0000234) Blood0.010 +/- 0.013 uMAbnormalAdolescent (13-18 years old)Male details
Epitestosterone (HMDB0000628) Blood0.00068 +/- 0.00004 uMAbnormalAdult (>18 years old)Male details
Hypomagnesemia 1, intestinal  (602014 )
MetaboliteBiospecimenConcentrationPatient StatusAgeSexDetails
Calcium (HMDB0000464) Blood2310 uMAbnormalAdolescent (13-18 years old)Male details
Calcium (HMDB0000464) Blood2090 uMAbnormalChildren (1-13 years old)Female details
Magnesium (HMDB0000547) Blood490 uMAbnormalAdolescent (13-18 years old)Male details
Magnesium (HMDB0000547) Blood560 uMAbnormalChildren (1-13 years old)Female details
Displaying diseases 326 - 350 of 660 in total