| HMDBP00439 | OGDH | 7p14-p13 | 2-oxoglutarate dehydrogenase, mitochondrial | Enzyme | 17 metabolites |
| HMDBP11578 | PHPT1 | | 14 kDa phosphohistidine phosphatase | Enzyme | 15 metabolites |
| HMDBP10653 | OGFOD1 | 16q12.2 | 2-oxoglutarate and iron-dependent oxygenase domain-containing protein 1 | Enzyme | 2 metabolites |
| HMDBP10654 | OGFOD2 | 12q24.31 | 2-oxoglutarate and iron-dependent oxygenase domain-containing protein 2 | Enzyme | 2 metabolites |
| HMDBP09100 | OGDHL | | 2-oxoglutarate dehydrogenase-like, mitochondrial | Enzyme | 13 metabolites |
| HMDBP09171 | YWHAB | 20q13.1 | 14-3-3 protein beta/alpha | Enzyme | 3 metabolites |
| HMDBP03089 | MOGAT2 | 11q13.5 | 2-acylglycerol O-acyltransferase 2 | Enzyme | 62056 metabolites |
| HMDBP00049 | GCAT | 22q13.1 | 2-amino-3-ketobutyrate coenzyme A ligase, mitochondrial | Enzyme | 5 metabolites |
| HMDBP01101 | UGT8 | 4q26 | 2-hydroxyacylsphingosine 1-beta-galactosyltransferase | Enzyme | 41 metabolites |
| HMDBP07284 | MOGAT3 | 7q22.1 | 2-acylglycerol O-acyltransferase 3 | Enzyme | 49313 metabolites |
| HMDBP09172 | YWHAG | 7q11.23 | 14-3-3 protein gamma | Enzyme | 2 metabolites |
| HMDBP01040 | DECR1 | 8q21.3 | 2,4-dienoyl-CoA reductase, mitochondrial | Enzyme | 3 metabolites |
| HMDBP04645 | MOGAT1 | 2q36.1 | 2-acylglycerol O-acyltransferase 1 | Enzyme | 49313 metabolites |
| HMDBP02428 | CNP | 17q21 | 2',3'-cyclic-nucleotide 3'-phosphodiesterase | Enzyme | 10 metabolites |
| HMDBP09413 | AGPAT6 | 8p11.21 | 1-acylglycerol-3-phosphate O-acyltransferase 6 (Lysophosphatidic acid acyltransferase, zeta), isoform CRA_b | Enzyme | 7072 metabolites |
| HMDBP01577 | AGPAT3 | 21q22.3 | 1-acyl-sn-glycerol-3-phosphate acyltransferase gamma | Enzyme | 7161 metabolites |
| HMDBP03003 | AGPAT5 | 8p23.1 | 1-acyl-sn-glycerol-3-phosphate acyltransferase epsilon | Enzyme | 7160 metabolites |
| HMDBP04526 | AGPAT4 | 6q26 | 1-acyl-sn-glycerol-3-phosphate acyltransferase delta | Enzyme | 7159 metabolites |
| HMDBP01579 | AGPAT2 | 9q34.3 | 1-acyl-sn-glycerol-3-phosphate acyltransferase beta | Enzyme | 7159 metabolites |
| HMDBP01581 | AGPAT1 | 6p21.3 | 1-acyl-sn-glycerol-3-phosphate acyltransferase alpha | Enzyme | 7159 metabolites |
| HMDBP00299 | BCKDHB | 6q14.1 | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial | Enzyme | 45 metabolites |
| HMDBP01508 | PDK3 | | [Pyruvate dehydrogenase [lipoamide]] kinase isozyme 3, mitochondrial | Enzyme | 3 metabolites |
| HMDBP00910 | HMGCR | 5q13.3-q14 | 3-hydroxy-3-methylglutaryl-coenzyme A reductase | Enzyme | 13 metabolites |
| HMDBP02552 | YWHAZ | 8q23.1 | 14-3-3 protein zeta/delta | Enzyme | 2 metabolites |
| HMDBP10676 | ADI1 | 2p25.3 | 1,2-dihydroxy-3-keto-5-methylthiopentene dioxygenase | Enzyme | 8 metabolites |