| HMDBP00315 | Galactocerebrosidase | P54803 | GALC | 14q31 | Enzyme | Not Available |
| HMDBP00316 | Arylsulfatase D | P51689 | ARSD | | Unknown | Not Available |
| HMDBP00318 | Galactosylceramide sulfotransferase | Q99999 | GAL3ST1 | 22q12.2 | Enzyme | Not Available |
| HMDBP00320 | Arylsulfatase A | P15289 | ARSA | 22q13.33 | Unknown | Not Available |
| HMDBP00324 | Arylsulfatase E | P51690 | ARSE | | Unknown | Not Available |
| HMDBP00434 | Globoside alpha-1,3-N-acetylgalactosaminyltransferase 1 | Q8N5D6 | GBGT1 | 9q34.13-q34.3 | Unknown | Not Available |
| HMDBP00557 | N-acetylglucosaminyl-phosphatidylinositol de-N-acetylase | Q9Y2B2 | PIGL | 17p12-p11.2 | Enzyme | Not Available |
| HMDBP00776 | Sphingomyelin phosphodiesterase | P17405 | SMPD1 | 11p15.4-p15.1 | Enzyme | Not Available |
| HMDBP00845 | Ceramide glucosyltransferase | Q16739 | UGCG | 9q31 | Enzyme | Not Available |
| HMDBP00874 | Lactosylceramide 4-alpha-galactosyltransferase | Q9NPC4 | A4GALT | 22q13.2 | Enzyme | Not Available |
| HMDBP00940 | Phosphatidylinositol N-acetylglucosaminyltransferase subunit Q | Q9BRB3 | PIGQ | 16p13.3 | Enzyme | Not Available |
| HMDBP00941 | Phosphatidylinositol N-acetylglucosaminyltransferase subunit A | P37287 | PIGA | Xp22.1 | Enzyme | Not Available |
| HMDBP00942 | Phosphatidylinositol N-acetylglucosaminyltransferase subunit H | Q14442 | PIGH | 14q24.1 | Enzyme | Not Available |
| HMDBP00943 | Phosphatidylinositol N-acetylglucosaminyltransferase subunit P | P57054 | PIGP | 21q22.2 | Enzyme | Not Available |
| HMDBP00944 | Phosphatidylinositol N-acetylglucosaminyltransferase subunit C | Q92535 | PIGC | 1q23-q25 | Enzyme | Not Available |
| HMDBP01084 | Acid ceramidase | Q13510 | ASAH1 | 8p22 | Enzyme | Not Available |
| HMDBP01089 | Ectonucleotide pyrophosphatase/phosphodiesterase family member 7 | Q6UWV6 | ENPP7 | 17q25.3 | Unknown | Not Available |
| HMDBP01090 | Sphingomyelin phosphodiesterase 2 | O60906 | SMPD2 | 6q21 | Unknown | Not Available |
| HMDBP01298 | Collagen type IV alpha-3-binding protein | Q9Y5P4 | COL4A3BP | 5q13.3 | Enzyme | Not Available |
| HMDBP01673 | Proactivator polypeptide | P07602 | PSAP | 10q21-q22 | Enzyme | - Rafi MA, Amini S, Zhang XL, Wenger DA: Correction of sulfatide metabolism after transfer of prosaposin cDNA to cultured cells from a patient with SAP-1 deficiency. Am J Hum Genet. 1992 Jun;50(6):1252-8. [PubMed:1350885 ]
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| HMDBP01719 | Ganglioside GM2 activator | P17900 | GM2A | 5q33.1 | Enzyme | Not Available |
| HMDBP01768 | Myelin basic protein | P02686 | MBP | 18q23 | Enzyme | - Maggio B, Yu RK: Interaction and fusion of unilamellar vesicles containing cerebrosides and sulfatides induced by myelin basic protein. Chem Phys Lipids. 1989 Oct;51(2):127-36. [PubMed:2480186 ]
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| HMDBP01795 | Glucosylceramidase | P04062 | GBA | 1q21 | Enzyme | Not Available |
| HMDBP02132 | P-selectin | P16109 | SELP | 1q22-q25 | Enzyme | - Squadrito F, Altavilla D, Squadrito G, Campo GM, Arlotta M, Quartarone C, Minutoli L, Ferlito M, Saitta A, Caputi AP: Sulfatide reduces leucocyte accumulation and reverts vascular failure in splanchnic artery occlusion shock. Eur J Pharmacol. 1998 Nov 13;361(1):101-8. [PubMed:9851547 ]
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| HMDBP02394 | L-selectin | P14151 | SELL | 1q23-q25 | Enzyme | - Kajihara J, Guoji Y, Kato K, Suzuki Y: Sulfatide, a specific sugar ligand for L-selectin, blocks CCl4-induced liver inflammation in rats. Biosci Biotechnol Biochem. 1995 Jan;59(1):155-7. [PubMed:7534512 ]
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